Enchondromatosis with cervical spine involvement in children: small series and review
https://doi.org/10.14531/ss2022.1.56-62
Abstract
Objective: to present different variants of the clinical course and surgical treatment of an extremely rare vertebral pathology – enchondromatosis with involvement of the cervical vertebrae in children. Two cases of local and multiple forms of bone dyschondroplasia with damage to the cervical vertebrae, accompanied by orthopedic and neurological complications in children aged 7 and 11, are described. As a result of the operation, complaints were completely stopped in one child and neurological disorders were eliminated in another. The diagnosis was verified histologically. The results were followed up for more than 2 years and 1 year after the operation, respectively. Present-day data on Ollie’s disease in children are presented. Indications, timing and volume of surgical intervention for bone dyschondroplasia are determined individually, depending on the size, location, and number of enchondromas. However, if the cervical spine involvement is complicated by increasing pain and neurological disorders, it is precisely decompression of the spinal cord that should be set as a priority aim of the surgery.
About the Authors
D. B. Malamashin
St. Petersburg Research Institute of Phthisiopulmonology
32 Politekhnicheskaya str., St. Petersburg, 194064, Russia
Russian Federation
Russian Federation
MD, PhD, orthopedic surgeon, senior researcher, Clinic of Pediatric Surgery and Orthopedics
A. Yu. Mushkin
St. Petersburg Research Institute of Phthisiopulmonology;
Pavlov First Saint Petersburg State Medical University
32 Politekhnicheskaya str., St. Petersburg, 194064, Russia;
6–8 L’va Tolstogo str., St. Petersburg, 197022, Russia
Russian Federation
Russian Federation
DMSc, Prof., chief researcher, Head of the Scientific and Clinical Centre for Spinal Pathology, Head of the Clinic of Pediatric Surgery and Orthopedics; Professor of the Department of traumatology and orthopedics
D. A. Glukhov
St. Petersburg Research Institute of Phthisiopulmonology
32 Politekhnicheskaya str., St Petersburg, 194064, Russia
Russian Federation
Russian Federation
postgraduate student, orthopedic surgeon
V. P. Snishchuk
Leningrad Regional Children’s Clinical Hospital;
St. Petersburg Research Institute of Phthisiopulmonology
6 Komsomola str., St. Petersburg, 195009, Russia;
32 Politekhnicheskaya str., St. Petersburg, 194064, Russia
Russian Federation
Russian Federation
neurosurgeon, chief external expert for pediatric neurosurgery of the Leningrad Region Healthcare Committee
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Review
For citations:
Malamashin D.B., Mushkin A.Yu., Glukhov D.A., Snishchuk V.P. Enchondromatosis with cervical spine involvement in children: small series and review. Russian Journal of Spine Surgery (Khirurgiya Pozvonochnika). 2022;19(1):56-62. https://doi.org/10.14531/ss2022.1.56-62
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