Preview

Russian Journal of Spine Surgery (Khirurgiya Pozvonochnika)

Advanced search

TREATMENT OF PATIENTS WITH CAUDAL REGRESSION SYNDROME

https://doi.org/10.14531/ss2011.3.56-59

Abstract

The paper presents clinical observation of a patient with a rare congenital malformation of the distal spine and spinal cord – the caudal regression syndrome. The patient showed an absence of the lumbosacral spinal segment with neurological disorders and contractures of the lower extremities. The patient underwent reconstructive vertebral pelvic fusion surgery. Surgical treatment resulted in elimination of the lumbosacral spine instability, correction of kyphotic deformity, and creation of support ability of the spine.

About the Authors

Sergey Valentinivich Vissarionov
Research Pediatric Orthopaedic Institute n.a. G.I.Turner, St.Petersburg
Russian Federation


Irina Vadimovna Kazarian
Research Pediatric Orthopaedic Institute n.a. G.I.Turner, St.Petersburg
Russian Federation


Sergey Mikhailovich Belyanchikov
Research Pediatric Orthopaedic Institute n.a. G.I.Turner, St.Petersburg
Russian Federation


References

1. Виссарионов С.В., Казарян И.В. Синдром каудальной регрессии // Хирургия позвоночника. 2010. № 2. С. 50–55.

2. Boulas MM. Recognition of caudal regression syndrome. Adv Neonatal Care. 2009;9:61–69.

3. Currarino G, Coln D, Votteler T. Triad of anorectal, sacral, and presacral anomalies. AJR Am J Roentgenol. 1981;137:395–398.

4. Dal Monte A, Andrisano A, Capanna R. The surgical treatment of lumbo-sacral coccygeal agenesis. Ital J Orthop Traumatol. 1979;5:259–266.

5. Guille JT, Benevides R, DeAlba CC. Lumbosacral agenesis: a new classification correlating spinal deformity and ambulatory potential. J Bone Joint Surg Am. 2002;84:32–38.

6. Harlow CL, Partington MD, Thieme GA. Lumbosacral agenesis: clinical characteristics, imaging, and embryogenesis. Pediatr Neurosurg. 1995;23:140–147.

7. Kaissi A, Klaushofer K, Grill F. Caudal regression syndrome and popliteal webbing in connection with maternal diabetes mellitus: a case report and literature review. Cases J. 2008;1:407.

8. Martucciello G, Torre M, Belloni E, et al. Currarino syndrome: proposal of a diagnostic and therapeutic protocol. J Pediatr Surg. 2004;39:1305–1311.

9. Renshaw TS. Sacral agenesis. J Bone Joint Surg Am. 1978;60:373–383.

10. Rieger MA, Hall JE, Dalury DF. Spinal fusion in a patient with lumbosacral agenesis. Spine. 1990;15:1382–1384.

11. Singh SK, Singh RD, Sharma A. Caudal regression syndrome – case report and review of literature. Pediatr Surg Int. 2005;21:578–581.

12. Tachdjian’s Pediatric Orthopaedics / Ed. by JA Herring. Elsevier, 2008:1466–1471.

13. Winter RB. Congenital absence of the lumbar spine and sacrum: one-stage reconstruction with subsequent two-stage spine lengthening. J Pediatr Orthop. 1991;11:666–670.

14. Welch JP, Aterman K. The syndrome of caudal dysplasia: a review, including etiologic considerations and evidence of heterogeneity. Pediatr Pathol. 1984;2:313–327.

15. Wilmshurst JM, Kelly R, Borzyskowski M. Presentation and outcome of sacral agenesis: 20 years’ experience. Dev Med Child Neurol. 1999;41:806–812.


Review

For citations:


Vissarionov S.V., Kazarian I.V., Belyanchikov S.M. TREATMENT OF PATIENTS WITH CAUDAL REGRESSION SYNDROME. Russian Journal of Spine Surgery (Khirurgiya Pozvonochnika). 2011;(3):056-059. (In Russ.) https://doi.org/10.14531/ss2011.3.56-59



Creative Commons License
This work is licensed under a Creative Commons Attribution 4.0 License.


ISSN 1810-8997 (Print)
ISSN 2313-1497 (Online)