KYPHOSCOLIOSIS CAUSED BY LYMPHANGIOGENIC FORM OF GORHAM - STOUT DISEASE WITH AXIAL SKELETAL LESION
https://doi.org/10.14531/ss2017.2.70-75
Abstract
The paper presents a clinical observation of a child with lymphangiogenic form of spontaneous osteolysis (Gorham - Stout disease) associated with massive destruction of the rib cage and progressive kyphoscoliotic deformity. Staged surgical treatment under the therapy with osteoclast inhibitors resulted in the deformity correction and significant improvement in the quality of life. The prognosis remains unclear due to the risk of osteolysis progression.
About the Authors
Aleksandr Yuryevich Mushkin
St. Petersburg Research Institute of Phthisiopulmonology; Mechnikov North-West State Medical University
Russian Federation
Russian Federation
Igor Aleksandrovich Komolkin
St. Petersburg Research Institute of Phthisiopulmonology; St. Petersburg State Pediatric Medical University
Russian Federation
Russian Federation
Mikhail Mikhailovich Kostik
St. Petersburg State Pediatric
Russian Federation
Russian Federation
Denis Borisovich Malamashin
St. Petersburg Research Institute of Phthisiopulmonology
Russian Federation
Russian Federation
References
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Review
For citations:
Mushkin A.Yu., Komolkin I.A., Kostik M.M., Malamashin D.B. KYPHOSCOLIOSIS CAUSED BY LYMPHANGIOGENIC FORM OF GORHAM - STOUT DISEASE WITH AXIAL SKELETAL LESION. Russian Journal of Spine Surgery (Khirurgiya Pozvonochnika). 2017;14(2):70-75. https://doi.org/10.14531/ss2017.2.70-75
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