Preview

Russian Journal of Spine Surgery (Khirurgiya Pozvonochnika)

Advanced search

SHORT-TERM RESULTS OF SURGICAL CORRECTION OF INFANTILE SCOLIOSIS ASSOCIATED WITH NEUROFIBROMATOSIS TYPE 1

https://doi.org/10.14531/ss2011.2.19-22

Abstract

Objective. To assess short-term results of a VEPTR instrumentation application for treatment of juvenile malignant progressing scoliotic deformity of the spine associated with neurofibromatosis type 1.

Material and Methods. Three patients aged 5.5 to 7 years were operated on for severe deformity of the spine associated with neurofibromatosis type 1. The mean age at the time of deformity detection was 3.5 years. Average magnitude of the primary scoliotic curve was 89.3°. Device configuration was varied depending on nature of the deformity.

Results. Primary scoliotic curvature was reduced after surgery down to 67°. Correction was 22.3° (25 %). Complications were not recorted.

Conclusion. The VEPTR instrumentation is a method of choice for controlled correction of infantile and juvenile deformities of the spine and thorax of various etiology.

About the Authors

Mikhail Vitalyevich Mikhailovsky
Novosibirsk Research Institute of Traumatology and Orthopaedics
Russian Federation


Vasily Aleksandrovich Suzdalov
Novosibirsk Research Institute of Traumatology and Orthopaedics
Russian Federation


Denis Nikolayevich Dolotin
Novosibirsk Research Institute of Traumatology and Orthopaedics
Russian Federation


References

1. Михайловский М.В., Зайдман А.М., Лебедева М.Н. Хирургическая коррекция деформаций позвоночника при нейрофиброматозе: опыт применения CDI // Хирургия позвоночника. 2008. № 3. С. 8–15.

2. Михайловский М.В., Суздалов В.А. Синдром торакальной недостаточности при инфантильном врожденном сколиозе // Хирургия позвоночника. 2010. № 3. С. 20–28.

3. Михайловский М.В., Ульрих Э.В., Суздалов В.А. и др. Инструментарий VEPTR в хирургии инфантильных и ювенильных сколиозов: первый отечественный опыт // Хирургия позвоночника. 2010. № 3. С. 31–41.

4. Поздникин Ю.И., Афанасьев А.П. Хирургическое лечение деформаций позвоночника у детей с незавершенным ростом при нейрофиброматозе // Адаптация различных систем организма при сколиотической деформации позвоночника. Методы лечения. М., 2003. С. 180–181.

5. Campbell R.M., Smith M.D., Hell-Vocke A.K. Expansion thoracoplasty: the surgical technique of opening-wedge thoracostomy. Surgical technique // J. Bone Joint Surg. Am. 2004. Vol. 86. Suppl. 1. P. 51–64.


Review

For citations:


Mikhailovsky M.V., Suzdalov V.A., Dolotin D.N. SHORT-TERM RESULTS OF SURGICAL CORRECTION OF INFANTILE SCOLIOSIS ASSOCIATED WITH NEUROFIBROMATOSIS TYPE 1. Russian Journal of Spine Surgery (Khirurgiya Pozvonochnika). 2011;(2):019-022. (In Russ.) https://doi.org/10.14531/ss2011.2.19-22



Creative Commons License
This work is licensed under a Creative Commons Attribution 4.0 License.


ISSN 1810-8997 (Print)
ISSN 2313-1497 (Online)