SURGICAL CORRECTION OF SUBAXIAL KYPHOSIS IN A CHILD WITH TYPE I NEUROFIBROMATOSIS: RARE CLINICAL CASE AND LITERATURE REVIEW
https://doi.org/10.14531/ss2018.2.12-17
Abstract
The paper presents a case of rapidly developing severe cervical kyphosis in a 5-year-old child which was the first clinical manifestation of type I neurofibromatosis (NF1). Surgical correction was carried out in two stages with preliminary hardware halo-traction and subsequent reconstruction of the spine using titanium mesh cage with bone autograft and posterior instrumentation. The deformity was corrected from the magnitude of 79° to the restoration of physiological lordosis. Long-term results were followed-up for 2.5 years with full maintenance of the achieved deformity correction. A 15-year literature review on the cervical spine lesions in NF1 is presented.
About the Authors
D. B. Malamashin
St. Petersburg Research Institute of Phthisiopulmonology
Russian Federation
Russian Federation
Denis Borisovich Malamashin - MD, PhD, senior researcher.
Politekhnicheskaya str., 32, 194064, St. Petersburg
M. M. Schelkunov
Mechnikov North-West State Medical University
Russian Federation
Russian Federation
Mikhail Mikhailovich Shchelkunov - clinical resident.
Piskarevsky ave., 47, 195067, St. Petersburg
M. A. Krasnikov
Regional Children’s Hospital
Russian Federation
Russian Federation
Maksim Alexandrovich Krasnikov – neurosurgeon.
Moskovskaya str., 6А, 398055, Lipetsk
A. Yu. Mushkin
St. Petersburg Research Institute of Phthisiopulmonology; Mechnikov North-West State Medical University
Russian Federation
Russian Federation
Aleksandr Yuryevich Mushkin - DMSc, Prof., chief researcher, «Extrapulmonary Tuberculosis» Prospect Research Coordinator, Head of Clinic of Pediatric Surgery and Orthopedics St. Petersburg RI Phthisiopulmonology; Professor of Pediatric Traumatology and Orthopaedics NW SMU n.a. I.I. Mechnikov.
Politekhnicheskaya str., 32, 194064, St. Petersburg; Piskarevsky ave., 47, 195067, St. Petersburg
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Review
For citations:
Malamashin D.B., Schelkunov M.M., Krasnikov M.A., Mushkin A.Yu. SURGICAL CORRECTION OF SUBAXIAL KYPHOSIS IN A CHILD WITH TYPE I NEUROFIBROMATOSIS: RARE CLINICAL CASE AND LITERATURE REVIEW. Russian Journal of Spine Surgery (Khirurgiya Pozvonochnika). 2018;15(2):12-17. https://doi.org/10.14531/ss2018.2.12-17
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