SURGICAL TREATMENT OF A PATIENT WITH MULTIPLE FRACTURES OF THE THORACIC AND LUMBAR VERTEBRAE ASSOCIATED WITH HAJDU – CHENEY SYNDROME
https://doi.org/10.14531/ss2019.1.25-31
Abstract
A clinical case of surgical and multimodal conservative treatment of an 11-year-old female patient with Hajdu – Cheney syndrome with multiple vertebral fractures in the thoracic and lumbar spine is presented. The main and significant manifestations of this syndrome are osteoporosis and acroosteolysis. After the injury, the child underwent correction of posttraumatic spinal deformity and stabilization of spinal motion segments by a placement of multi-anchor instrumentation through a posterior approach. The long-term postoperative period was characterized by the absence of bone block formation, development of distal junctional kyphosis and scoliotic deformity, which required additional surgical intervention in the amount of elongation of instrumentation and correction of the developed curvature. The paper describes in detail the clinical manifestations of the syndrome, the results of surgical treatment, and clinical and radiological characteristics.
About the Authors
S. V. Vissarionov
The Turner Scientific Research Institute for Children’s Orthopaedics;
North-Western State Medical University n.a. I.I. Mechnikov
Russian Federation
Russian Federation
Sergei Valentinovich Vissarionov, DMSc, Prof., Deputy director for science and academic work, head of research of the Department of spine pathology and neurosurgery
professor of Department of pediatric traumatology and orthopaedics
A. N. Filippova
The Turner Scientific Research Institute for Children’s Orthopaedics
Russian Federation
Aleksandra Nikolaevna Filippova, postgraduate student
Russian Federation
Aleksandra Nikolaevna Filippova, postgraduate student
M. V. Zhurbitskaia
The Turner Scientific Research Institute for Children’s Orthopaedics
Russian Federation
Maria Vyacheslavovna Zhurbitskaia, clinical resident
Russian Federation
Maria Vyacheslavovna Zhurbitskaia, clinical resident
N. O. Khusainov
The Turner Scientific Research Institute for Children’s Orthopaedics
Russian Federation
Nikita Olegovich Khusainov, MD, PhD, orthopedic traumatologist, researcher of the Department of spine pathology and neurosurgery
Russian Federation
Nikita Olegovich Khusainov, MD, PhD, orthopedic traumatologist, researcher of the Department of spine pathology and neurosurgery
S. M. Belyanchikov
The Turner Scientific Research Institute for Children’s Orthopaedics
Russian Federation
Sergei Mikhailovich Belyanchikov, MD, PhD, orthopedic traumatologist, head of the Department of spine pathology and neurosurgery
Russian Federation
Sergei Mikhailovich Belyanchikov, MD, PhD, orthopedic traumatologist, head of the Department of spine pathology and neurosurgery
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Review
For citations:
Vissarionov S.V., Filippova A.N., Zhurbitskaia M.V., Khusainov N.O., Belyanchikov S.M. SURGICAL TREATMENT OF A PATIENT WITH MULTIPLE FRACTURES OF THE THORACIC AND LUMBAR VERTEBRAE ASSOCIATED WITH HAJDU – CHENEY SYNDROME. Russian Journal of Spine Surgery (Khirurgiya Pozvonochnika). 2019;16(1):25-31. https://doi.org/10.14531/ss2019.1.25-31
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